Weight | 190.155 g/mol |
---|---|
Formula | C6H10N2O5 |
Hydrogen Acceptors | 3 |
Hydrogen Donors | 4 |
Aromatic Rings | 0 |
Rotatable Bonds | 5 |
Carglumic acid (1188-38-1)
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- Sigma-Aldrich - Carglumic acid159.00 - 338.10 USD
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- New developments in the treatment of hyperammonemia: emerging use of carglumic acid (International Journal of General Medicine, 2011)
- Role of carglumic acid in the treatment of acute hyperammonemia due to N-acetylglutamate synthase deficiency (Therapeutics and Clinical Risk Management, 2011)
- Carglumic acid: an additional therapy in the treatment of organic acidurias with hyperammonemia? (Orphanet Journal of Rare Diseases, 2008)
- Use of carglumic acid in the treatment of hyperammonaemia during metabolic decompensation of patients with propionic acidaemia. (Molecular Genetics and Metabolism, 2013)
- Carglumic acid approved to treat genetic hyperammonemia (American Journal of Health-system Pharmacy, 2010)
- Carglumic acid enhances rapid ammonia detoxification in classical organic acidurias with a favourable risk-benefit profile: a retrospective observational study (Orphanet Journal of Rare Diseases, 2016)
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Including Acute Oral Tox, Skin Sensitization, Eye Irritation, Aquatic Tox, & more. -
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- Pubchem - Carglumic acid
- Wikipedia - carglumic acid
Carglumic acid is an orphan drug, marketed by Orphan Europe under the trade name Carbaglu. Carglumic acid is used for the treatment of hyperammonaemia in patients with N-acetylglutamate synthase deficiency. The initial daily dose ranges from 100 to 250mg/kg, adjusted thereafter to maintain normal plasma levels of ammonia.
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